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Hirayama disease in females

Web1 feb 2024 · Introduction. Initially reported in 1959 and named after its founder, Hirayama disease (HD) is also known as juvenile amyotrophy of the distal upper extremity or cervical flexion myelopathy, with the characteristic of having a benign and self-limiting process.1, 2 With less than 1000 reported cases in the literature, this rare disease is most prevalent … Web10 apr 2024 · Thalassemia is identified as a prevalent disease in Malaysia, known to be one of the developing countries. Fourteen patients with confirmed cases of thalassemia were recruited from the Hematology Laboratory. The molecular genotypes of these patients were tested using the multiplex-ARMS and GAP-PCR methods. The samples were repeatedly …

The clinical characteristics of Hirayama disease in females

Web28 dic 2024 · Hirayama disease results in focal amyotrophy of upper limbs. It is seen in young Asian males. Distal upper limbs are usually involved in an asymmetric manner and patients can have cold paresis. Neck MRI in flexion shows dural changes and spinal cord signals in a proportion of patients. Cervical segments can be relatively long in such patients. Web17 mar 2016 · Hirayama et al. originally reported this clinical entity in 1959, and called it “juvenile muscular atrophy of unilateral upper extremity” [ 1 ]. This disease is characterized by muscle wasting and weakness, affecting predominantly the lower cervical myotomes [ 2 ]. It affects mostly young males in their teens and twenties. fb mendoza llc https://theeowencook.com

Severe cervical flexion myelopathy with long tract signs: a ... - Nature

Web1 gen 2024 · Objectives: Hirayama disease is a rare myelopathy, occurring predominantly in males with onset in the teens. Methods and results: Here, we report a young female … Web10 ago 2024 · Hirayama disease (HD), also known as juvenile benign muscular atrophy of the upper extremities, or monomelic amyotrophy (MMA), is characterized by muscular … WebAlthough females presented with Hirayama disease two years earlier than males, no other clinical differences were observed. Hirayama disease is likely associated with growth … horaire train temara tanger

Juvenile muscular atrophy of the distal upper limb (Hirayama disease ...

Category:Cervical Spine MR Imaging Findings of Patients with Hirayama Disease …

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Hirayama disease in females

Pathogens Free Full-Text Iliopsoas Muscle Weakness as a Key ...

Web遗传性压力易感性周围神经病（hereditary neuropathy with liability to pressure palsies，HNPP）是一种遗传性运动感觉性神经病，呈常染色体显性遗传，其神经病理特征性改变为髓鞘增厚形成“腊肠体”样结构，因此，曾被称为腊肠体样周围神经病 [1] 。 HNPP的主要症状表现为与压力相关的反复发作性肢体麻木无力。 WebHirayama, K.Non-progressive juvenile spinal muscular atrophy of the distal upper limb (Hirayama’s disease). In: De Jong, J, editor. Handbook of clinical neurology. Amsterdam: Elsevier; 1991. p. 107–20. Google Scholar 3 3. Misra, UK, Kalita, J, …

Hirayama disease in females

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Web18 mag 2024 · Hirayama is a rare, nonfamiliar, monomelic amyotrophy originally described by Dr. Hirayama in 1959.[1] Classical findings include muscle atrophy and weakness of the forearms and hands, either unilateral or bilateral, and without sensory loss. This usually progresses for one or two years before plateauing and eventually showing an abrupt … Web1 set 2024 · Adolescent female Case report 1. Introduction Hirayama disease is a rare and benign motor neuron disorder that involves a single upper extremity which was originally …

Web1 nov 2011 · Hirayama disease (juvenile muscular atrophy of distal upper extremity) is a cervical myelopathy. Predominantly affecting male adolescents, it is characterized by progressive muscular weakness and... Web1 gen 2024 · Hirayama disease is a relatively unusual cause of cervical myelopathy characterized by uni- or bilateral asymmetric weakness, fasciculations and atrophy of the …

WebAlthough females presented with Hirayama disease two years earlier than males, no other clinical differences were observed. Hirayama disease is likely associated with growth and development in puberty, and early identification, regardless of whether patients are male or female, is critical to optimizing prognosis. © Web1 feb 2024 · Hirayama disease (HD), also known as juvenile benign muscular atrophy of the upper extremities, or juvenile cervical flexion myelopathy, is characterized by the juvenile onset of unilateral or asymmetric amyotrophy and weakness of …

WebHirayama disease (juvenile muscular atrophy of distal upper extremity) is a cervical myelopathy. Predominantly affecting male adolescents, it is characterized by progressive muscular weakness and atrophy of distal upper limbs, followed by spontaneous arrest within several years. Although the cause o …

Web8 lug 2016 · Eight patients (6 males, 2 females; age range 15–23 years) with clinical suspicion of Hirayama disease underwent clinical, electrophysiological and MRI diagnostic evaluation between January 2007 and November 2013 at University Hospital Federico II, Naples, Italy. We obtained written informed consent from all of our patients. fb mekaWeb5 apr 2024 · 1 BACKGROUND. Chronic kidney disease (CKD) is a significant public health issue, 1 About 37 million adult Americans have CKD, according to the Centers for Disease Control and Prevention and prevalence projections indicate that they will rise as the population ages and the obesity and diabetes epidemics spread, 2, 3 although end-stage … fb meloWeb1 ago 2024 · Discussion Although females presented with Hirayama disease two years earlier than males, no other clinical differences were observed. Hirayama disease is … horaire train temara kenitraWeb31 gen 2011 · Introduction: The purpose of this study was to compare the pattern of hand muscle involvement in Hirayama disease (HD) and amyotrophic lateral sclerosis (ALS). Methods: We reviewed findings of upper limb nerve conduction studies of 46 HD patients and 60 ALS patients. The findings from 54 healthy subjects were used for comparison. horaire tv dakar 2022Web13 apr 2024 · Human T-cell leukemia virus-1 (HTLV-1)-associated myelopathy/tropical spastic paraparesis (HAM/TSP) is a slowly progressive neurological disease that arises from HTLV-1 infection. Pathologically, the condition is characterized by diffuse myelitis, which is most evident in the thoracic spinal cord. Clinical manifestations of the infectious … horaire tram besançon ginkoWeb28 nov 2024 · Hirayama disease is a relatively unusual cause of cervical myelopathy characterized by uni- or bilateral asymmetric weakness, fasciculations and atrophy of the … fb metlabsWeb1 feb 2013 · EMG : electromyography HD : Hirayama Disease LOA : loss of attachment To characterize the MR imaging findings of North American patients with HD, we reviewed neutral and flexion cervical MR imaging examinations performed for possible HD at 3 academic medical centers located in the Southeastern, Southwestern, and Midwestern … horaire train rabat tanger